%0 Generic %A Nappi, Luigi %A Vasciaveo, Lorenzo %A Sorrentino, Felice %A Scutiero, Gennaro %A Iannone, Piergiorgio %A Greco, Pantaleo %D 2019 %T Fetal Noncompaction Cardiomyopathy and Histologic Diagnosis of Spongy Myocardium: Case Report and Review of the Literature %U https://scielo.figshare.com/articles/dataset/Fetal_Noncompaction_Cardiomyopathy_and_Histologic_Diagnosis_of_Spongy_Myocardium_Case_Report_and_Review_of_the_Literature/7562522 %R 10.6084/m9.figshare.7562522.v1 %2 https://scielo.figshare.com/ndownloader/files/14053724 %2 https://scielo.figshare.com/ndownloader/files/14053727 %K noncompaction cardiomyopathy %K spongy myocardium %K left ventricular noncompaction cardiomyopathy %X

Abstract Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in their isolated form, are rare cardiomyopathies. They are characterized by a thickened myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae. This condition is associated with a variable clinical phenotype including heart failure, thromboembolism, and sudden death. We report a case of LVNC at 26 weeks and 4 days of gestation revised on the basis of what is currently reported in the literature. A review of the literature was performed to better describe this rare condition. Left ventricular noncompaction is a rare fetal condition and it should be suspected in case of cardiomyopathy.

%I SciELO journals